PULSATING EXOPHTHALMOS

Pulsating Exophthalmos Due to Neurofibromatosis.

CASES of pulsating exophthalmos, which are seen from time to time, are mostly vascular in origin. Rarely they are due to transmitted cerebral pulsations, as in congenital failure of the orbital roof, erosion of the walls due to inflammatory processes, and traumatic hiatus of the orbital roof. Occasionally they are due to plexiform neurofibromatosis. von Recklinghausen (1882) first described a c...

Pulsating exophthalmos in von Recklinghausen's disease.

Unilateral pulsating exophthalmos is often due to an arteriovenous communication between the internal carotid artery and the cavernous sinus, or to an arteriovenous aneurysm in the orbit between the ophthalmic arteries and veins. Occasionally a true aneurysm of the ophthalmic artery may cause exophthalmos. Trauma to the head is a common aetiological factor, but the condition may arise spontaneo...

[On the spontaneous cure of a case of pulsating exophthalmos].

Reconstruction of the sphenoid wing in a case of neurofibromatosis type 1 and complex unilateral orbital dysplasia with pulsating exophthalmos.

Sphenoid wing dysplasia is a defining feature of neurofibromatosis type 1 (NF1). This defect of the skull base can be associated with pulsating exophthalmos. This report describes the successful reconstruction of a dysplastic sphenoid wing in an NF1 patient using lateral orbitotomy as a scarcely visible and sufficiently extendable approach. An intraoperative computed cone-beam computed tomograp...

Intermittent exophthalmos.

The syndrome of intermittent exophthalmos classically consists of enophthalmos with the head in the upright position, and exophthalmos which develops rapidly in one eye (usually the left) when venous stasis is induced by bending or lowering the head, turning the head forcibly, hyperextension of the neck, coughing, forced expiration with or without compression of the nostrils, or pressure on the...